Upadacitinib for Treatment-Resistant Urticarial Vasculitis: A Case Study and Therapeutic Insight

Upadacitinib for Treatment-Resistant Urticarial Vasculitis: A Case Study and Therapeutic Insight

Authors

  • Francesca Falcinelli Department of Medical, Surgical and Neurological Science, Dermatology Section, University of Siena, S. Maria alle Scotte Hospital, Siena, Italy https://orcid.org/0000-0002-3149-8695
  • Edoardo Conticini Rheumatology Unit, Department of Medicine, Surgery and Neurosciences, University of Siena, Italy
  • Luca Cantarini Rheumatology Unit, Department of Medicine, Surgery and Neurosciences, University of Siena, Italy
  • Bruno Frediani Rheumatology Unit, Department of Medicine, Surgery and Neurosciences, University of Siena, Italy
  • Pietro Rubegni Dermatology Unit and Skin Bank, Department of Medical, Surgical and Neurosciences, Siena University Hospital, Siena – Italy
  • Laura Calabrese Dermatology Unit and Skin Bank, Department of Medical, Surgical and Neurosciences, Siena University Hospital, Siena – Italy; Institute of Dermatology, Catholic University of the Sacred Heart, Rome, Italy

Keywords:

urticarial vasculitis, upadacitinib, jak-inhibitors, Janus Kinase Inhibitors

References

Marzano AV, Maronese CA, Genovese G, et al. Urticarial vasculitis: Clinical and laboratory findings with a particular emphasis on differential diagnosis. J Allerg Clin. 2022; 149: 1137–1149. DOI:10.1016/j.jaci.2022.02.007.

Mohamed MF, Bhatnagar S, Parmentier JM, et al. Upadacitinib: Mechanism of action, clinical, and translational science. Clinic Transl Sci. 2024; 17: e13688. DOI:10.1111/cts.13688.

Mansouri P, Mozafari N, Chalangari R, Martits‐Chalangari K. Efficacy of oral tofacitinib in refractory chronic spontaneous urticaria and urticarial vasculitis. Dermatol Ther. 2022; 35. DOI:10.1111/dth.15932.

Zhu K-J, Yang P-D, Xu Q. Tofacitinib Treatment of Refractory Cutaneous Leukocytoclastic Vasculitis: A Case Report. Front Immunol. 2021; 12: 695768. DOI:10.3389/fimmu.2021.695768

Rathore U, Thakare DR, Patro P, et al. A systematic review of clinical and preclinical evidences for Janus kinase inhibitors in large vessel vasculitis. Clin Rheumatol 2022; 41: 33–44. DOI:10.1007/s10067-021-05973-4.

Ebata A, Ogawa-Momohara M, Fukaura R, et al. Increased Janus kinase activation in cutaneous vasculitis. J Am Acad Dermatol. 2024; 90: 627–629. DOI:10.1016/j.jaad.2023.10.056.

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Published

2025-04-30

How to Cite

1.
Falcinelli F, Conticini E, Cantarini L, Frediani B, Rubegni P, Calabrese L. Upadacitinib for Treatment-Resistant Urticarial Vasculitis: A Case Study and Therapeutic Insight. Dermatol Pract Concept. 2025;15(2):5139. doi:10.5826/dpc.1502a5139

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