Periumbilical perforating pseudoxanthoma elasticum: a rare case report

Periumbilical perforating pseudoxanthoma elasticum: a rare case report

Authors

  • Abhijeet K. Jha Department of Skin & VD, Patna Medical College and Hospital, Patna, Bihar, India
  • MD Zeeshan Department of Skin & VD, Patna Medical College and Hospital, Patna, Bihar, India
  • Binod K. Sinha Department of Skin & VD, Patna Medical College and Hospital, Patna, Bihar, India
  • Anupama Singh Department of Skin & VD, Patna Medical College and Hospital, Patna, Bihar, India
  • Pallavi Agrawal Department of Pathology, Patna Medical College and Hospital, Patna, Bihar, India

Keywords:

periumbilical perforating pseudoxanthoma elasticum (PPPXE), dermoscopy

Abstract

Periumbilical perforating pseudoxanthoma elasticum (PPPXE) usually presents with well-defined periumbilical yellowish atrophic plaques with keratotic papules at the periphery. It is considered a variant of hereditary pseudoxanthoma elasticum or a localized acquired cutaneous dermatosis. The lesions usually occur in the periumbilical area in obese, multiparous women. Here, we report an additional case of periumbilical perforating pseudoxanthoma elasticum with its dermoscopic features.

 

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Published

2018-04-30

Issue

Section

Observation

How to Cite

1.
Jha AK, Zeeshan M, Sinha BK, Singh A, Agrawal P. Periumbilical perforating pseudoxanthoma elasticum: a rare case report. Dermatol Pract Concept. 2018;8(1). Accessed May 10, 2026. https://dpcj.org/index.php/dpc/article/view/dermatol-pract-concept-articleid-dp0802a02

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